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Title

Anesthesia management in a young child with aromatic l-amino acid decarboxylase deficiency
Authors
Vutskits, Laszlo
Menache Starobinski, Caroline
Manzano, Sergio
Haenggeli, Charles-André
Habre, Walid
Published in Paediatric Anaesthesia. 2006, vol. 16, no. 1, p. 82-4
Abstract Aromatic l-amino acid decarboxylase (AADC) deficiency is characterized by an almost complete absence of sympathetic autoregulation, because of very low levels of circulating catecholamines. Here, we report the successful management of four consecutive anesthesia procedures in a young child presenting with AADC deficiency. Our experience suggests that, with appropriate anticipation of the potential autonomic disturbances, anesthesia, at least for minor surgical and diagnostic procedures, can be conducted safely in patients with AADC deficiency.
Keywords Anesthesia, General — Anesthetics, Inhalation — Aromatic-L-Amino-Acid Decarboxylases/deficiency — Child, Preschool — Female — Humans — Infant — Methyl Ethers
Identifiers
PMID: 16409536
Full text
Article (Published version) (56 Kb) - document accessible for UNIGE members only Limited access to UNIGE
Structures
Faculté de médecine / Section de médecine clinique / Département d'anesthésiologie, pharmacologie et soins intensifs
Faculté de médecine / Section de médecine clinique / Département de pédiatrie
Research group Enfants et hyperréactivité bronchique (69)
Citation
(ISO format) 		VUTSKITS, Laszlo et al. Anesthesia management in a young child with aromatic l-amino acid decarboxylase deficiency. In: Paediatric Anaesthesia, 2006, vol. 16, n° 1, p. 82-4. https://archive-ouverte.unige.ch/unige:46896

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Deposited on : 2015-02-19

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