Expert management of congenital portosystemic shunts and their complications

Mclin, Valérie Anne; Franchi-Abella, Stéphanie; Bruetsch, Timothee; Bahadori, Atessa; Casotti, Valeria; de Ville de Goyet, Jean; Dumery, Grégoire; Gonzales, Emmanuel; Guérin, Florent; Hascoet, Sebastien; Heaton, Nigel; Kuhlmann, Béatrice; Lador, Frédéric; Lambert, Virginie; Marra, Paolo; Plessier, Aurélie; Quaglia, Alberto; Rougemont-Pidoux, Anne-Laure; Savale, Laurent; Sarma, Moinak Sen; Sitbon, Olivier; Superina, Riccardo Antonio; Uchida, Hajime; van Albada, Mirjam; Johannes van der Doef, Hubert Petrus; Vilgrain, Valérie; Wacker Bou Puigdefabregas, Julie Caroline; Zwaveling, Nitash; Debray, Dominique; Wildhaber, Barbara

doi:10.1016/j.jhepr.2023.100933

Scientific article

Review

Open access

English

Expert management of congenital portosystemic shunts and their complications

CollaboratorsCalinescu-Tuleasca, Ana Maria; Gadiri, Mehdi Ali; Martinelli Diaz Valentin, Josefina; Ricoeur, Alexis; Rock, Nathalie; Steger, Vanessa

Published inJHEP reports, vol. 6, no. 1, 100933

Errata

Erratum in : McLin VA, Franchi-Abella S, Brütsch T, Bahadori A, Casotti V, de Ville de Goyet J, Dumery G, Gonzales E, Guérin F, Hascoet S, Heaton N, Kuhlmann B, Lador F, Lambert V, Marra P, Plessier DA, Quaglia A, Rougemont AL, Savale L, Sarma MS, Sitbon O, Superina RA, Uchida H, van Albada M, Johannes van der Doef HP, Vilgrain V, Wacker J, Zwaveling-Soonawala N, Debray D, Wildhaber BE. Corrigendum to "Expert management of congenital portosystemic shunts and their complications" [JHEP Reports 6 (2024)]. JHEP Rep. 2024 Jan 30;6(3):101024
DOI : 10.1016/j.jhepr.2024.101024
PMID : 38481635

Publication date2024-01

First online date2023-10-20

Abstract

Congenital portosystemic shunts are often associated with systemic complications, the most challenging of which are liver nodules, pulmonary hypertension, endocrine abnormalities, and neurocognitive dysfunction. In the present paper, we offer expert clinical guidance on the management of liver nodules, pulmonary hypertension, and endocrine abnormalities, and we make recommendations regarding shunt closure and follow-up.

Keywords

Adenoma
Congenital portosystemic shunt
Focal nodular hyperplasia
Hepatocellular carcinoma
Hyperandrogenism
Hyperinsulinism
Hypoglycemia
Occlusion test
Portal pressure
Puberty
Pulmonary hypertension
Β-catenin

Affiliation

Research group

Citation (ISO format)

MCLIN, Valérie Anne et al. Expert management of congenital portosystemic shunts and their complications. In: JHEP reports, 2024, vol. 6, n° 1, p. 100933. doi: 10.1016/j.jhepr.2023.100933