Expert management of congenital portosystemic shunts and their complications

Article Article scientifique Revue de la littérature Expert management of congenital portosystemic shunts and their complications eng 2023-10-20 2024-01 author Mclin Valérie Anne Swiss Pediatric Liver Center, Gastroenterology, Hepatology and Pediatric Nutrition Unit, Department of Pediatrics, Gynecology and Obstetrics, University of Geneva, Geneva, Switzerland.,ERN RARE LIVER. 799651 Département de Pédiatrie, Gynécologie et Obstétrique (PETRI) author Franchi-Abella Stéphanie Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.,AP-HP, Centre de référence des maladies rares du foie de l'enfant, Service de radiologie pédiatrique diagnostique et interventionnelle, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.,BIOMAPS UMR 9011 CNRS, INSERM, CEA, Orsay, France.,ERN RARE LIVER.,ERN Transplant Child. author Bruetsch Timothee Communication in Science, rue du Tunnel 7, Carouge, Switzerland. 539895 author Bahadori Atessa Department of Pediatrics, Gynecology and Obstetrics, University of Geneva, Geneva, Switzerland. 691412 author Casotti Valeria Pediatric Hepatology, Gastroenterology and Transplant Centre, ASST Papa Giovanni XXIII Hospital, Bergamo, Italy.,ERN Transplant Child. author de Ville de Goyet Jean Pediatric Department for the Treatment and Study of Abdominal Diseases and Abdominal Transplantation, ISMETT UPMC, Palermo, Italy. author Dumery Grégoire Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.,AP-HP, Service de gynécologie et d'obstétrique, Hôpital Bicêtre, Le Kremlin-Bicêtre, France. author Gonzales Emmanuel Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.,AP-HP, Centre de référence des maladies rares du foie de l'enfant, FHU Hepatinov, Service d'hépatologie et transplantation hépatique pédiatriques, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.,INSERM UMRS_1193, Orsay, France.,ERN RARE LIVER.,ERN Transplant Child. author Guérin Florent Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.,AP-HP, Service de chirurgie pédiatrique, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.,ERN RARE LIVER.,ERN Transplant Child. author Hascoet Sebastien Department of Congenital Heart Diseases, Hôpital Marie Lannelongue, France.,INSERM UMR_S 999, Université Paris, France. author Heaton Nigel Institute of Liver Studies, Kings College Hospital, London, England. author Kuhlmann Béatrice Pediatric Endocrinology, Cantonal Hospital Aarau KSA, Aarau, Switzerland. author Lador Frédéric Service de Pneumologie, University of Geneva, Geneva, Switzerland. 89384 Département de médecine (DEMED) author Lambert Virginie Cardiologie congénitale, Institut Mutualiste Montsouris, Paris, France.,AP-HP, Centre de référence des maladies rares du foie de l'enfant, Service de radiologie pédiatrique diagnostique et interventionnelle, Hôpital Bicêtre, Le Kremlin-Bicêtre, France. author Marra Paolo Department of Radiology, Papa Giovanni XXIII Hospital, School of Medicine and Surgery - University of Milano-Bicocca, Bergamo, Italy. author Plessier Aurélie Centre de référence des maladies vasculaires du foie, Service d'hépatologie Hôpital Beaujon, Clichy, France.,ERN RARE LIVER.,VALDIG. author Quaglia Alberto Department of Cellular Pathology, Royal Free London NHS Foundation Trust/UCL Cancer Institute, London, England. author Rougemont-Pidoux Anne-Laure Swiss Pediatric Liver Center, Division of Clinical Pathology, Diagnostic Department, University of Geneva, Geneva, Switzerland. 29140 Département de pathologie et immunologie (PATIM) author Savale Laurent Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.,AP-HP, Centre de référence de l'hypertension pulmonaire, Service de pneumologie et soins intensifs respiratoires, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.,INSERM UMR_S 999, Hôpital Marie Lannelongue, Le Plessis Robinson, France.,ERN Lung. author Sarma Moinak Sen Department of Pediatric Gastroenterology, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, India. author Sitbon Olivier Université Paris-Saclay, Faculté de médecine, Le Kremlin-Bicêtre, France.,AP-HP, Centre de référence de l'hypertension pulmonaire, Service de pneumologie et soins intensifs respiratoires, Hôpital Bicêtre, Le Kremlin-Bicêtre, France.,INSERM UMR_S 999, Hôpital Marie Lannelongue, Le Plessis Robinson, France.,ERN Lung. author Superina Riccardo Antonio Northwestern University Feinberg School of Medicine, Ann & Robert H. Lurie Children's Hospital of Chicago, Chicago, Illinois, USA. author Uchida Hajime Organ Transplantation Center, National Center for Child Health and Development, Tokyo, Japan. author van Albada Mirjam Department of paediatric and congenital cardiology, University Medical Center Groningen, University of Groningen, The Netherlands. author Johannes van der Doef Hubert Petrus Division of paediatric gastroenterology and hepatology, Department of paediatrics, University Medical Center Groningen, Groningen, The Netherlands. author Vilgrain Valérie Université Paris Cité, CRI, INSERM, Paris, France.,AP-HP, Département de Radiologie, Hôpital Beaujon. Nord, Clichy, France.,ERN RARE LIVER.,VALDIG. author Wacker Bou Puigdefabregas Julie Caroline Pediatric Cardiology Unit, Department of pediatrics, Gynecology and Obstetrics, University of Geneva, Geneva, Switzerland.,Centre Universitaire Romand de Cardiologie et Chirurgie Cardiaque Pédiatrique, University of Geneva and Lausanne, Switzerland. 540977 author Zwaveling Nitash Department of Pediatric Endocrinology, Amsterdam University Medical Centers, University of Amsterdam, Amsterdam, The Netherlands. author Debray Dominique AP-HP, Unité d'hépatologie pédiatrique et transplantation hépatique, Hôpital Necker, Paris, France.,Centre de Référence des maladies rares du foie de l'enfant, FILFOIE, France.,ERN RARE LIVER.,ERN Transplant Child. author Wildhaber Barbara Swiss pediatric Liver Center, Division of pediatric surgery, Department of Pediatrics, Gynecology, and Obstetrics, University of Geneva, Geneva, Switzerland.,ERN RARE LIVER. 595596 Département de Pédiatrie, Gynécologie et Obstétrique (PETRI) collaborator Calinescu-Tuleasca Ana Maria 766852 collaborator Gadiri Mehdi Ali 906803 collaborator Martinelli Diaz Valentin Josefina 401877 collaborator Ricoeur Alexis 983348 collaborator Rock Nathalie 826963 collaborator Steger Vanessa 817859 100933 10.1016/j.jhepr.2023.100933 38234409 2589-5559 PMC10792643 https://www.sciencedirect.com/science/article/pii/S2589555923002641 Congenital portosystemic shunts are often associated with systemic complications, the most challenging of which are liver nodules, pulmonary hypertension, endocrine abnormalities, and neurocognitive dysfunction. In the present paper, we offer expert clinical guidance on the management of liver nodules, pulmonary hypertension, and endocrine abnormalities, and we make recommendations regarding shunt closure and follow-up. Adenoma Congenital portosystemic shunt Focal nodular hyperplasia Hepatocellular carcinoma Hyperandrogenism Hyperinsulinism Hypoglycemia Occlusion test Portal pressure Puberty Pulmonary hypertension Β-catenin Dewey 616.0757 Dewey 616 Dewey 616.07 Dewey 618 56 Département de médecine 221 58 Département de pédiatrie, gynécologie et obstétrique 223 137 Département de pathologie et immunologie 21F 62 Département de radiologie et informatique médicale 227 false 559 Pathologies hépatiques congénitales et acquises de l'enfant 900 546 Recherche clinique en chirurgie pédiatrique 886 179 L'hypertension pulmonaire (pédiatrie) 228 JHEP reports 6 1 c9bc32f7-287b-4284-8e2e-b167538448d4 Article (Published version) Public Article-scientifique-from-europePmc.pdf 2180418 application/pdf CC BY-4.0 129812a528173d4a568b6ea7f0d433bb3260423ca8560c191971bb0458985662 9c49fc09-8565-4a44-a9de-3eb28ec3a41a Supplemental data Public ScienceDirect_files_18Mar2024_10-32.zip 5410213 application/zip 7a62eade19cf24c1be2e3010ada92453781a9f6a85ec078454f2b717e7593e86 99258852-aa5b-4212-b73e-8ad832fd59d7 Corrigendum Public 1-s2.0-S2589555924000259-main.pdf 330659 application/pdf 8a6634d1f3e024d90cf940e552c5f496661dcf4c27881a0a05c637fcd1e8620c It has come to our attention that we did not include the full surname of one of the authors in our publication. ‘Nitash Zwaveling’ should read ‘Nitash Zwaveling-Soonawala’. We apologise for any inconvenience caused. 10.1016/j.jhepr.2024.101024 38481635 openAccess Faculté de médecine / Section de médecine clinique / Département de médecine Faculté de médecine / Section de médecine clinique / Département de pédiatrie, gynécologie et obstétrique Faculté de médecine / Section de médecine fondamentale / Département de pathologie et immunologie Faculté de médecine / Section de médecine clinique / Département de radiologie et informatique médicale

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