Scientific article
English

Lymphocytic leiomyositis and myenteric ganglionitis are intrinsic features of cystic fibrosis: studies in distal intestinal obstruction syndrome and meconium ileus

Published in

Journal of pediatric gastroenterology and nutrition, vol. 49, no. 1, p. 42-51

Publication date

2009

Abstract

Cystic fibrosis (CF) is a multisystem disorder intrinsically associated with inflammation of mucosal surfaces. Because inflammation can result in enteric neuromuscular dysfunction we hypothesized that terminal ileitis in patients with CF may predispose to distal ileal obstruction syndrome (DIOS).

Keywords

  • Adolescent
  • Child
  • Child, Preschool
  • Crohn Disease/complications/physiopathology
  • Cystic Fibrosis/complications/physiopathology
  • Duodenum/physiopathology
  • Female
  • Fibroblasts/pathology
  • Ganglion Cysts/physiopathology
  • Humans
  • Ileum/physiopathology
  • Ileus/complications
  • Infant
  • Inflammation/etiology/physiopathology
  • Intestinal Atresia/complications
  • Intestinal Mucosa/physiopathology
  • Intestinal Pseudo-Obstruction/etiology/physiopathology
  • Lymphocytes
  • Male
  • Manometry
  • Meconium
  • Muscle Cells/metabolism/pathology
  • Myenteric Plexus/physiopathology
  • Retrospective Studies

Citation (ISO format)

SMITH, Virpi V et al. Lymphocytic leiomyositis and myenteric ganglionitis are intrinsic features of cystic fibrosis: studies in distal intestinal obstruction syndrome and meconium ileus. In: Journal of pediatric gastroenterology and nutrition, 2009, vol. 49, n° 1, p. 42–51. doi: 10.1097/MPG.0b013e318186d35a

Main files (1)

Article (Published version)

Identifiers

Journal ISSN

0277-2116
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Technical informations

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07/10/2014 15:38:00

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07/10/2014 15:38:00

Update

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