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Persistence of the intestinal defect in abetalipoproteinaemia after liver transplantation |
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Published in | European journal of pediatrics. 1998, vol. 157, no. 7, p. 576-8 | |
Abstract | A 16-year-old girl is described with abetalipoproteinaemia who underwent liver transplantation for hepatic cirrhosis. After this procedure her serum lipoprotein profile was corrected; however, fat malabsorption and steatorrhea persisted because the primary defect, a mutant microsomal triglyceride-transfer protein, remains expressed in the intestine. | |
Keywords | Abetalipoproteinemia/complications/metabolism/surgery — Adolescent — Carrier Proteins/metabolism — Female — Humans — Intestines/metabolism — Liver Cirrhosis/etiology/surgery — Liver Transplantation | |
Identifiers | PMID: 9686820 | |
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Research groups | Gastroentérologie et transplantation (pédiatrie) (181) Hépatologie chirurgicale (327) | |
Citation (ISO format) | BRAEGGER, C et al. Persistence of the intestinal defect in abetalipoproteinaemia after liver transplantation. In: European journal of pediatrics, 1998, vol. 157, n° 7, p. 576-8. doi: 10.1007/s004310050882 https://archive-ouverte.unige.ch/unige:41296 |