en
Scientific article
Case report
Open access
English

Symptomatic syringomyelia occurring as a late complication of posterior fossa medulloblastoma removal in infancy in a boy also suffering from scaphocephaly

Published inChild's nervous system, vol. 25, no. 12, p. 1633-1637
Collection
  • Open Access - Licence nationale Springer
Publication date2009
Abstract

INTRODUCTION: The association of a medulloblastoma and a syringomyelia has been already described in rare instances albeit without symptoms related to the syrinx. CASE REPORT: The case of a 23-year-old man operated in infancy for a medulloblastoma and then treated solely with adjuvant chemotherapy is reported. He was also operated in infancy for a scaphocephaly. With a very long time delay, he has developed a Chiari I and a symptomatic cervico-dorsal syringomyelia. The symptoms attributed to the syrinx consisted of a unilateral prurigo over the left arm which was so severe to lead to self-mutilation. DISCUSSION: Clinical and magnetic resonance imaging follow-up after cervico-dorsal decompression shows a significant improvement of the symptoms together with a reduction of the size of the syrinx. This case is discussed in the light of the presumed pathophysiology of the syrinx and its exceptional clinical presentation.

Keywords
  • Arnold-Chiari Malformation/diagnosis/etiology/surgery
  • Cranial Fossa, Posterior/pathology/*surgery
  • Craniosynostoses/*complications/surgery
  • Craniotomy/*adverse effects
  • Decompression, Surgical
  • Humans
  • Infant
  • Magnetic Resonance Imaging
  • Male
  • Medulloblastoma/complications/pathology/*surgery
  • Skull Base Neoplasms/complications/pathology/*surgery
  • Syringomyelia/*diagnosis/etiology/surgery
  • Young Adult
Citation (ISO format)
EL HASSANI, Yassine et al. Symptomatic syringomyelia occurring as a late complication of posterior fossa medulloblastoma removal in infancy in a boy also suffering from scaphocephaly. In: Child’s nervous system, 2009, vol. 25, n° 12, p. 1633–1637. doi: 10.1007/s00381-009-0968-6
Main files (1)
Article (Published version)
accessLevelPublic
Identifiers
ISSN of the journal0256-7040
549views
254downloads

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