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Symptomatic syringomyelia occurring as a late complication of posterior fossa medulloblastoma removal in infancy in a boy also suffering from scaphocephaly

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Published in Child's Nervous System. 2009, vol. 25, no. 12, p. 1633-1637
Abstract INTRODUCTION: The association of a medulloblastoma and a syringomyelia has been already described in rare instances albeit without symptoms related to the syrinx. CASE REPORT: The case of a 23-year-old man operated in infancy for a medulloblastoma and then treated solely with adjuvant chemotherapy is reported. He was also operated in infancy for a scaphocephaly. With a very long time delay, he has developed a Chiari I and a symptomatic cervico-dorsal syringomyelia. The symptoms attributed to the syrinx consisted of a unilateral prurigo over the left arm which was so severe to lead to self-mutilation. DISCUSSION: Clinical and magnetic resonance imaging follow-up after cervico-dorsal decompression shows a significant improvement of the symptoms together with a reduction of the size of the syrinx. This case is discussed in the light of the presumed pathophysiology of the syrinx and its exceptional clinical presentation.
Keywords Arnold-Chiari Malformation/diagnosis/etiology/surgeryCranial Fossa, Posterior/pathology/*surgeryCraniosynostoses/*complications/surgeryCraniotomy/*adverse effectsDecompression, SurgicalHumansInfantMagnetic Resonance ImagingMaleMedulloblastoma/complications/pathology/*surgerySkull Base Neoplasms/complications/pathology/*surgerySyringomyelia/*diagnosis/etiology/surgeryYoung Adult
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PMID: 19662425
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EL HASSANI, Yassine et al. Symptomatic syringomyelia occurring as a late complication of posterior fossa medulloblastoma removal in infancy in a boy also suffering from scaphocephaly. In: Child's Nervous System, 2009, vol. 25, n° 12, p. 1633-1637. https://archive-ouverte.unige.ch/unige:19791

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Deposited on : 2012-04-23

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