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Scientific article
Case report
Open access
English

Pericardiectomy and mechanical mitro-aortic valve replacement in a young patient with Erdheim-Chester disease

Published inTexas Heart Institute journal, vol. 51, no. 1, 238201
Publication date2024-02-07
Abstract

Erdheim-Chester disease is a rare histiocytosis that primarily affects the skeletal system, but cardiovascular manifestations occur in 75% of cases and are associated with a poor prognosis. Given the small number of cases, the evolution and management of the disease are uncertain. Therefore, it is important to report and share Erdheim-Chester cases. This report presents the case of a young patient with constrictive pericarditis and mitral valve regurgitation resulting from Erdheim-Chester disease.

eng
Keywords
  • Erdheim-Chester disease
  • Aortic valve
  • Mitral valve
  • Pericardiectomy
  • Pericarditis, constrictive
Citation (ISO format)
LOPEZ PEREZ, Nerea et al. Pericardiectomy and mechanical mitro-aortic valve replacement in a young patient with Erdheim-Chester disease. In: Texas Heart Institute journal, 2024, vol. 51, n° 1, p. 238201. doi: 10.14503/THIJ-23-8201
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Article (Published version)
Identifiers
ISSN of the journal0730-2347
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