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Scientific article
Case report
Open access
English

Surgical management of vascular Ehlers-Danlos syndrome and its challenges: a case report

Published inSwiss Medical Weekly, vol. 150, w20379
Publication date2020
Abstract

Ehlers-Danlos syndrome (EDS) is a heterogeneous group of rare inherited diseases involving connective tissue. Vascular EDS (vEDS) is associated with abnormal type III collagen, which is an essential component of skin, hollow organs and arterial walls, and causes potentially fatal visceral and arterial complications. The surgical management of these patients is challenging and should be limited to life-saving procedures.

Keywords
  • Vascular Ehlers-Danlos syndrome
  • Aneurysm
  • Dissection
  • Colonic stenosis
  • Haemorrhage
Citation (ISO format)
DA SOUSA, Francisco et al. Surgical management of vascular Ehlers-Danlos syndrome and its challenges: a case report. In: Swiss Medical Weekly, 2020, vol. 150, p. w20379. doi: 10.4414/smw.2020.20379
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Article (Published version)
Identifiers
ISSN of the journal1424-7860
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Technical informations

Creation12/17/2020 11:10:00 AM
First validation12/17/2020 11:10:00 AM
Update time03/16/2023 12:11:11 AM
Status update03/16/2023 12:11:10 AM
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