Progressive skin fibrosis is associated with a decline in lung function and worse survival in patients with diffuse cutaneous systemic sclerosis in the European Scleroderma Trials and Research (EUSTAR) cohort

Wu, Wanlong; Jordan, Suzana; Graf, Nicole; de Oliveira Pena, Janethe; Curram, John; Allanore, Yannick; Matucci-Cerinic, Marco; Pope, Janet E; Denton, Christopher P; Khanna, Dinesh; Distler, Oliver; EUSTAR

doi:10.1136/annrheumdis-2018-213455

Scientific article

English

Progressive skin fibrosis is associated with a decline in lung function and worse survival in patients with diffuse cutaneous systemic sclerosis in the European Scleroderma Trials and Research (EUSTAR) cohort

ContributorsWu, Wanlong; Jordan, Suzana; Graf, Nicole; de Oliveira Pena, Janethe; Curram, John; Allanore, Yannick; Matucci-Cerinic, Marco; Pope, Janet E; Denton, Christopher P; Khanna, Dinesh; Distler, Oliver; EUSTAR

CollaboratorsChizzolini, Carlo; Allali, Danièle

Published inAnnals of the Rheumatic Diseases, vol. 78, no. 5, p. 648-656

Publication date2019

Abstract

To determine whether progressive skin fibrosis is associated with visceral organ progression and mortality during follow-up in patients with diffuse cutaneous systemic sclerosis (dcSSc).

Keywords

Adult
Cohort Studies
Databases
Factual
Disease Progression
Europe
Female
Fibrosis
Humans
Kaplan-Meier Estimate
Lung/physiopathology
Male
Middle Aged
Scleroderma
Diffuse/complications/mortality/pathology
Severity of Illness Index
Skin/pathology
Skin Diseases/etiology/mortality/physiopathology
Survival Analysis
Time Factors

Affiliation entities

Faculté de médecine / Section de médecine fondamentale / Département de pathologie et immunologie

Citation (ISO format)

WU, Wanlong et al. Progressive skin fibrosis is associated with a decline in lung function and worse survival in patients with diffuse cutaneous systemic sclerosis in the European Scleroderma Trials and Research (EUSTAR) cohort. In: Annals of the Rheumatic Diseases, 2019, vol. 78, n° 5, p. 648–656. doi: 10.1136/annrheumdis-2018-213455

Article (Published version)

CC BY-NC

Identifiers

PID : unige:139862
DOI : 10.1136/annrheumdis-2018-213455
PMID : 30852552

Journal ISSN0003-4967

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Creation07/08/2020 10:27:00

First validation07/08/2020 10:27:00

Update15/03/2023 22:26:30

Status update15/03/2023 22:26:29

Last indexation31/10/2024 19:28:29

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Progressive skin fibrosis is associated with a decline in lung function and worse survival in patients with diffuse cutaneous systemic sclerosis in the European Scleroderma Trials and Research (EUSTAR) cohort

To determine whether progressive skin fibrosis is associated with visceral organ progression and mortality during follow-up in patients with diffuse cutaneous systemic sclerosis (dcSSc).

Technical informations