A facial inflammatory myofibroblastic tumour in a 6-year-old girl: plastic surgery lessons from a rare case

Article Article scientifique Méta-analyse A facial inflammatory myofibroblastic tumour in a 6-year-old girl: plastic surgery lessons from a rare case eng 2011 author Modarressi Ghavami Seyed Ali 105647 author Pietramaggiori Giorgio 667254 author Bezzola Thierry Laurent 90573 author Lacroix Sylvain 525655 author Richter Michel Willy 29907 author Rilliet Bénédict 50793 author Pittet Cuenod Brigitte Maud 114581 141-144 10.1016/j.jcms.2010.11.015 21194962 1010-5182 Inflammatory myofibroblastic tumours (IMT) are rare, challenging lesions with respect to differential diagnosis, biological behaviour and treatment. We reviewed the literature and report a unique case of a large (9 × 8 × 8 cm) IMT in the nasal region of a 6-year-old girl responsible for important facial deformation. Following surgical resection, without any craniofacial reconstruction, the dysmorphism regressed spontaneously with a good result at 2 years of follow-up. To date, this is the largest IMT reported. Surprisingly, after simple excision of the tumour the craniofacial bones and soft tissues regained spontaneously their normal anatomical position only after a few months. The bone plasticity was likely due to the young age of patient and the preservation of periosteum and muscles during the surgical excision. We conclude that a conservative approach may be considered as alternative to reconstructive surgery in particular cases in young subjects. Bone Regeneration Child Facial Bones/growth & development Facial Neoplasms/pathology/radiography/surgery Female Granuloma, Plasma Cell/pathology/radiography/surgery Humans Myofibroblasts/pathology Neoplasm Recurrence, Local/radiography/surgery Neoplasms, Muscle Tissue/pathology/radiography/surgery Treatment Outcome Dewey 616.8 Dewey 617 Swiss National Science Foundation L'effet de l'ischémie sur la différenciation et le fonctionnement des myofibroblastes cutanés 120571 CH Project funding 57 Département de chirurgie 222 61 Département des neurosciences cliniques 226 false 72 Groupe Pittet Cuenod Brigitte (chirurgie plastique et reconstructive) 96 555 Groupe Scolozzi Paolo (chirurgie maxillo-faciale et buccale) 896 Journal of cranio-maxillo-facial surgery 39 2 d1ad7075-57f4-4660-9f13-4a3fcea5db4a Article (Published version) Restricted 2011_modarressi_j_craniomaxillofac_surg.pdf 794224 application/pdf restrictedAccess Faculté de médecine / Section de médecine clinique / Département de chirurgie Faculté de médecine / Section de médecine clinique / Département des neurosciences cliniques

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A facial inflammatory myofibroblastic tumour in a 6-year-old girl: plastic surgery lessons from a rare case	Journal of cranio-maxillo-facial surgery			2011	654	2

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Bezzola, Thierry Laurent